Spinal intradural primary malignant peripheral nerve sheath tumor with leptomeningeal seeding: Case report and literature review

Baharvahdat, H. and Ganjeifar, B. and Roshan, N. M. and Baradaran, A. (2018) Spinal intradural primary malignant peripheral nerve sheath tumor with leptomeningeal seeding: Case report and literature review. Turkish Neurosurgery, 28 (2). pp. 317-322.

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Abstract

Spinal intradural primary malignant peripheral nerve sheath tumors (MPNST) are rare in patients without neurofibromatosis. Here we represent a 3-year-old girl of primary intradural spinal malignant peripheral nerve sheath tumor. The tumor was removed partially and MPNST was diagnosed in the histopathological examination. Her condition deteriorated due to acute hydrocephalus in the following days. In this article, we discuss the clinical presentation, imaging, treatment, and prognosis of our patient and the other 22 patients of primary intradural MPNST, found in the literature. The Kaplan-Meier method was applied for univariate analysis and Cox proportional hazards model for multivariate analysis. This analysis showed that age, was an important factor predicting short-term survival of patients with MPNST. © 2018, Turk Neurosurg.

Item Type: Article
Additional Information: Cited By :2 Export Date: 16 February 2020 CODEN: TUNEE Correspondence Address: Baradaran, A.; Orthopedic Research Center, Ghaem Hospital, Mashhad University of Medical SciencesIran; email: Aslan.Baradaran@gmail.com
Uncontrolled Keywords: Hydrocephalus Malignant peripheral nerve sheath tumor Spinal intradural tumor carcinomatous meningitis case report female human nerve sheath tumor pathology preschool child secondary spinal cord tumor Child, Preschool Humans Meningeal Carcinomatosis Nerve Sheath Neoplasms Spinal Cord Neoplasms
Subjects: WL Nervous system
QZ pathology-neoplasms-Genetics
Divisions: Mashhad University of Medical Sciences
Depositing User: lib2 lib2 lib2
Date Deposited: 06 Jun 2020 07:25
Last Modified: 06 Jun 2020 07:25
URI: http://eprints.mums.ac.ir/id/eprint/17226

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