Phacoemulsification in bilateral anterior lenticonus in Alport syndrome: A case report

Sedaghat, M. R. and Momeni-Moghaddam, H. and Haghighi, B. and Moshirfar, M. (2019) Phacoemulsification in bilateral anterior lenticonus in Alport syndrome: A case report. Medicine (United States), 98 (39).

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Rationale:To report the visual status and results of phacoemulsification cataract surgery in a young patient with Alport syndrome associated with bilateral anterior lenticonus. The milestone of this report is the use of anterior segment optical coherence tomography (AS-OCT) to confirm the central protrusion of the anterior surface of the crystalline lens.Patient concerns:A 23-year-old young woman presented with severe progressive visual loss in both eyes, which started several years ago.Diagnoses:Refractive status was indicative of high myopia with astigmatism and vision was not improved with optimal correction to better than 0.1 in the right eye and 0.2 in the left eye (visual acuities given in decimal notation). Slit-lamp examination showed transparent cornea, anterior lenticonus and posterior sub-capsular cataract in both eyes. The classical appearance of oil droplet was evident using retro-illumination on the slit lamp.Interventions:The natural lenses were replaced with intraocular lens (IOL).Outcomes:An excellent refractive status achieved associated with an uncorrected distance visual acuity 0.9 and 0.8 in the right and left eye, respectively.Lessons:AS-OCT is a valuable device for confirming the budging of the anterior crystalline lens surface. © 2019 the Author(s). Published by Wolters Kluwer Health, Inc.

Item Type: Article
Additional Information: Export Date: 16 February 2020 CODEN: MEDIA Correspondence Address: Moshirfar, M.; John A. Moran Eye Center, Department of Ophthalmology and Visual Sciences, School of MedicineUnited States; email:
Uncontrolled Keywords: Alport syndrome anterior segment optical coherence tomography cataract crystalline lens lenticonus betamethasone adult Article astigmatism case report clinical article corrected distance visual acuity drug dose titration female high myopia human intraocular pressure lens implantation low vision phacoemulsification priority journal slit lamp microscopy vision visual acuity young adult diagnostic imaging lens capsule lens cortex nephritis optical coherence tomography pathology Humans Lens Capsule, Crystalline Lens Cortex, Crystalline Nephritis, Hereditary Tomography, Optical Coherence Vision, Low
Subjects: W General medicine- Health professions
Divisions: Mashhad University of Medical Sciences
Depositing User: mr lib1 lib1
Date Deposited: 27 Jun 2020 05:38
Last Modified: 27 Jun 2020 05:38

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